CJA
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
This Article
Right arrow Full Text (PDF)
Right arrow Submit a scholarly reply
Right arrow Alert me when this article is cited
Right arrow Alert me when eLetters are posted
Right arrow Alert me if a correction is posted
Services
Right arrow Similar articles in this journal
Right arrow Alert me to new issues of the journal
Right arrow Download to citation manager
Right arrow reprints & permissions
Citing Articles
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by NAGUIB, M.
Right arrow Articles by IBRAHIM, A. E. W.
Right arrow Search for Related Content
PubMed
Right arrow Articles by NAGUIB, M.
Right arrow Articles by IBRAHIM, A. E. W.

Canadian Journal of Anesthesia, Vol 33, 66-70, Copyright © 1986 by Canadian Anesthesiologists' Society

Clinical Reports: Anaesthetic Considerations in Klippel-Feil Syndrome

MOHAMED NAGUIB MB BCH MSC1, HESHAM FARAG MB BCH FFARCS1, and ABD EL WAHAB IBRAHIM MB BCH FRCS1

1 Departments of Anesthesiology and Neurosurgery, King Faisal University, King Fahd Hospital, P.O. Box 2208, Al-Khobar, Saudi Arabia, 31952

Address correspondence to: Dr. M. Naguib.

Anaesthesia for the repair of a large occipito cervical encephalomyelocele in a neonate with Kippel-Feil syndrome is described. The fusion of the cervical spines, a short neck, low posterior hair line and Sprengel's deformity, which were present in this patient, collectively indicated Klippel-Feil syndrome. In addition to the usual stigmata of the syndrome, this patient had a large encephalomyelocele and persistant patent ductus arteriosus complicated by congestive heart failure. Patients with this syndrome are vulnerable to cervical spinal cord injury and are at high risk for neurological injury not only during laryngoscopy and intubation but thereafter. Implications of Kippel-Feil syndrome for the anaesthetist are reviewed and discussed.

Key Words: ANAESTHESIA: paediatric • COMPLICATIONS: Klippel-Feil syndrome • GENETIC FACTORS: congenital defects






HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
Copyright © 1986 by the Canadian Anesthesiologists' Society.